Abstract

ROZAS REYES, P; SENARIS GONZALEZ, A  and  GONZALEZ RODRIGUEZ, CM. Orbit Xanthogranulomatosis: Erdheim-Chester disease. Arch Soc Esp Oftalmol [online]. 2004, vol.79, n.10, pp.515-518. ISSN 0365-6691.

Case report: A patient was studied because of upper lid bilateral edema and xanthelasmae-like lesions after three years of evolution. During the ophthalmologic examination orange-yellowish lesions and two symmetrical tumours were observed on the temporal part of both upper lids. Corticoid-therapy was undertaken which reduced the size of the tumours, however the size increased again after the discontinuation of treatment. A biopsy was performed and lid xanthogranulomatosis was diagnosed. Other systemic examinations were normal. Discussion: Erdheim-Chester disease is a xanthogranulomatosis that can affect ocular and periorbital structures. Combination of xanthelasmae-like lesions and bilateral orbital masses should make us consider this process and try to locate any associated systemic conditions.

Keywords : Xanthogranulomatosis; Erdheim-Chester disease.