Abstract

MEJIAS-MANZANO, María-de-los-Ángeles et al. IgG4-related sclerosing mesenteritis, a rare condition that causes abdominal pain. Rev. esp. enferm. dig. [online]. 2018, vol.110, n.3, pp.201-203. ISSN 1130-0108.  https://dx.doi.org/10.17235/reed.2018.5228/2017.

The identification of IgG4-related disease as a distinct immune-mediated condition encompassing disorders that were traditionally seen as idiopathic has been a revolution in the diagnostic and therapeutic algorithm in several medical fields. This condition usually involves multiple organs (isolated organ involvement is uncommon except in the pancreas) with characteristic histopathological findings. We report a case that was assessed due to abdominal pain and subsequently diagnosed with IgG4-related sclerosing mesenteritis. A comprehensive work-up of the case ruled out other conditions and a diagnosis of IgG4-related sclerosing mesenteritis was made according to radiographic and histopathological criteria.

Keywords : IgG4-related disease; IgG4-related sclerosing mesenteritis; Abdominal pain; Storiform fibrosis; IgG4 plasma cells.

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