Abstract

GARCIA-SERRANO, Guillermo et al. Fibrodysplasia ossificans progressiva: the role of oral and maxillofacial surgeon. Experience in two cases. Rev Esp Cirug Oral y Maxilofac [online]. 2014, vol.36, n.2, pp.73-77. ISSN 2173-9161.  https://dx.doi.org/10.1016/j.maxilo.2012.04.006.

The ossificans progressive fibrodysplasia is a rare genetic disorder that is characterized by the association of congenital malformations and progressive heterotopic ossification outbreaks since the early years of life. The scanty number of patients who suffer the disease, does that the course and treatment of the same one is not known for many specialists, in spite of the importance of the multidisciplinary managing of these patients. We present 2 cases evaluated by our service in the last 12 months; two 40 and 23-year-old males diagnosed in childhood with ossificans progressive fibrodysplasia who attended the maxilofacial surgery department for evaluation and treatment.

Keywords : Progressive fibrodysplasia ossificans; Congenital connective tissue disorders; Bone morphogenetic protein.

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