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Revista Española de Enfermedades Digestivas
versión impresa ISSN 1130-0108
Resumen
SUAREZ-SANCHEZ, Aida; SOLAR-GARCIA, Lorena; GARCIA-BERNARDO, Carmen y MIYAR-DE-LEON, Alberto. Lower gastrointestinal bleeding as a form of presentation in an adult case of Abernethy syndrome. Rev. esp. enferm. dig. [online]. 2018, vol.110, n.10, pp.667-668. ISSN 1130-0108. https://dx.doi.org/10.17235/reed.2018.5615/2018.
We report the case of a 29-year-old patient who presented with a short history of lower gastrointestinal bleeding. A diagnosis of Abernethy syndrome was made (congenital extrahepatic portosystemic shunt) after this uncommon clinical presentation. The prevalence of this congenital malformation is very low and usually manifests during the pediatric age, according to previously published reports.