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Revista Española de Cirugía Oral y Maxilofacial

On-line version ISSN 2173-9161Print version ISSN 1130-0558


CHAURAND-LARA, Jorge; PACHECO-RUIZ, Laura  and  MENDEZ-ROSITO, Diego. Malignant peripheral nerve sheath tumours as the source of orofacial pain. Rev Esp Cirug Oral y Maxilofac [online]. 2016, vol.38, n.3, pp.167-170. ISSN 2173-9161.

Malignant peripheral nerve sheath tumours (MPNSTs), also called neurofibrosarcomas or malignant schwannomas, represents 10% of all soft tissue sarcomas. The tumour is usually found in the lower extremities, and only 10 to 20% of all lesions occur in head and neck region, thus making it a rare entity. Neurofibroma is one of the common nerve sheath tumours occurring in the soft tissues, and generally appears in neurofibromatosis 1 or Von Recklinghausen's disease. Individuals with a family history of neurofibromatosis 1 are reported to have an increased risk of developing MPNSTs in their lifetime. However, this association is not seen in MPNSTs of the cranial nerves. In this study, the authors reviewed the current literature on MPNSTs of the trigeminal nerve to analyse the presentations, treatment options, and outcomes for patients with this disease, as well as the report of a case involving the 3 branches of the trigeminal nerve.

Keywords : Schwannoma; Malignant peripheral nerve tumour; Trigeminal.

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