Oncología (Barcelona)
ISSN 0378-4835
GUERRERO ZOTANO, A. et al. Carcinomatosis peritoneal por tumor apendicular. []. , 28, 4, pp.35-39. ISSN 0378-4835.
PURPOSE: Mucinous ascites by mucus-producing tumour epithelial cells with peritoneum dissemination is a rare condition known as pseudomyoma peritonaei. In nearly all the cases the cause is a primary tumour of the appendix. It is an entity with multifocal peritoneal epithelial implants, distributed in a characteristic way. Although it can be not aggressive histologically, it is invariably fatal clinically. MATERIAL AND METHODS: We present the case of a woman diagnosed of peritoneal carcinomatosis by an appendicular carcinoma, who was treated by surgery and systemic chemotherapy based on 5-FU. With this approach we got a long survival with a good symptomatic control. CONCLUSION: There are no standard treatments for this disease. Based on its particular behaviour, the approach of some specialists is an aggressive surgery combined with intraperitoneal chemotherapy. However, it is a complex procedure, not validated by clinical studies. Our case shows that it can be achieved a good clinical control with conservative surgery and systemic chemotherapy.
: Pseudomyxoma peritonaei; Appendiceal tumour; Peritoneal carcinomatosis.