Abstract

FIGUEIREDO, M.C.; FAUSTINO-SILVA, D.D.; BEZ, A.S.  and  RINCON, D.P.C.. Oral manifestations of Mobius syndrome associated to the Poland anomaly: a case report. Av Odontoestomatol [online]. 2009, vol.25, n.4, pp.179-183. ISSN 2340-3152.

The Mobius syndrome is a congenital paralysis of the sixth and seventh cranial nerves. It is characterized by craniofacial and limb malformations. When it is associated to the Poland, the Mobius syndrome shows aplasia of the pectoral muscle (Poland anomaly) and abnormalities of the feet and hands. The syndrome shows important oral and facial abnormalities like gothic palate, open bite, dry mouth, bifid uvula, tongue alterations, and because of this, there is the necessity of an effective odontological approach in order to establish an adequate oral health and patient's quality of life. In this study, the clinical case report shows the oral and general clinical aspects, as well as the odontological treatment made in a patient who has the Mobius/Poland syndrome. After the approach focus on the orientations to the carer and in the control of the periodontal and carie diseases, it was realized a significative reduction in the visible plaque index (VPI) and gum bleeding index (GBI). Currently, the patient is in maintenance. The syndrome is incurable; therefore, the treatment is based on the control and maintenance of oral manifestations.

Keywords : Poland syndrome; Mobius Syndrome; Oral manifestations; oral health.

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