Abstract

MARIN BOTERO, M.L. et al. Hypohydrotic ectodermal dysplasia: Report of cases. Av Odontoestomatol [online]. 2013, vol.29, n.1, pp.11-23. ISSN 2340-3152.

Ectodermal Hypohidrotic Dysplasia (EHD) is a genodermatosis characterized by the presence of the ectoderm-derived structures alterations and often the triad is given: Hypohidrosis, Hypotrichosis and hypodontia. The purpose of this article is to present 6 clinic cases attended in the Clinic of the Children Dental Care of the Faculty of dentistry of the University of Antioquia between 1998 and 2011. It´s document the oral and facial characteristics in this pathology in a family with inheritance associated with the X chromosome. For the treatment of this syndrome a protocol of management in multidisciplinary and integral form is proposed.

Keywords : Ectodermal dysplasia; hypohidrotic; hypotrichosis; hypodontia.

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