Abstract

ASENSIO-SANCHEZ, VM  and  CALVO-CRESPO, MJ. Orbital involvement as the first manifestation of Hand-Schuller-Christian disease: A case report. Arch Soc Esp Oftalmol [online]. 2005, vol.80, n.8, pp.483-486. ISSN 0365-6691.

Purpose/Material and Method: To describe the clinical case of a 20-month-old boy with Hand-Schuller-Christian disease. Exophthalmos was the only systemic manifestation evident over a period of at least 6 weeks, but later the triad of exophthalmos with multiple lytic lesions of the skull and diabetes insipidus were present. Results/Conclusion: Histiocytosis X should be considered in the differential diagnosis of orbital tumors in children.

Keywords : Exophthalmos; Hand-Schuller-Cristian; histiocytosis X.