Abstract

GUTIERREZ GOMEZ, C.; CERVANTES DIAZ, J. P.; MENENDEZ ARZAC, R.  and  MORALES NAYA, D. E.. Upper lip "ruffle deformity" correction in Melkerson- Rosenthal's syndrome. Cir. plást. iberolatinoam. [online]. 2009, vol.35, n.1, pp.79-84. ISSN 1989-2055.

Melkersson-Rosenthal Syndrome is a rare entity characterized by granulomatous orofacial swelling, recurrent facial palsy and lingua plicata. It's monosyntomatic form affecting only lips is known as Miescher granulomatous cheilitis. Many conservative treatments have been proposed to resolve the swelling; however many times they present recurrence or fail to respond. The surgical correction permit permanent improvement and better appearance. The surgical posterior reduction cheiloplastry removing mucosa and submucosa all along the lip proposed by several authors, gives the lips an stigma of the " ruffle" aspect; this is because there is no shortening of the total length of the previously enlarged lip because of the granulomatous swelling. We report the correction of this deformity by total thickness resection of the middle third of the lip which resolve this deformity. In this patient, we also report the involve of the neck which gave him the deformity of "iguana neck", resolved by direct resection and liposuction. The neck involvement in this pathology was not previously reported in the literature.

Keywords : Melkersson-Rosental syndrome; Surgical treatment.

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