Abstract

MARTIN-MENJIVAR, E.; GAXIOLA-GARCIA, M.A.; DUARTE Y SANCHEZ, A.J.  and  LUGO-BELTRAN, I.. Pollicization in Nager Syndrome: a case report. Cir. plást. iberolatinoam. [online]. 2015, vol.41, n.2, pp.197-202. ISSN 1989-2055.  https://dx.doi.org/10.4321/S0376-78922015000200012.

Treatment paradigm for a child with thumb deficiency or hypoplasia is based on severity, apart from other clinical features. Pollicization or surgical substitution of the thumb, most commonly using the index finger, is reserved for the most severe cases. We present the case of a 4-year-old male with Nager Syndrome. Among the most notable clinical characteristics we found: cleft palate, bilateral microtia, downslanting palpebral fissure, malar hypoplasia, mandibular hypoplasia, lower eyelid coloboma, partial tibial agenesis as well as bilateral hypoplastic/absent thumbs. Pollicization was performed for the right hand without complications. After 18 months follow-up, adequate cilyndrical and spherical grasp was achieved, as well as lateral prehension and opposition to fifth finger.

Keywords : Nager Syndrome; Acrofacial dysostosis; Thumb absent; Thumb hypoplastic; Hand congenital deformity.

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