Resumen

PIPA VALLEJO, A; GONZALEZ GARCIA, M; LOPEZ-ARRANZ MONJE, E  y  FERNANDEZ TORAL, J. Incontinentia Pigmenti. Odontostomatologics considerations: Prevention and therapeutic. Av Odontoestomatol [online]. 2005, vol.21, n.4, pp.211-215. ISSN 2340-3152.

Incontinentia pigmenti is a rare, family disorder of genetic transmisión linked to the X chromosome which appears almost exclusively in females; it causes skin disorders and anomalies that affect hair, teeth, eyes and the central nervous system. Teeth are affected in 50-80% of patients. Patients are late in teething, some or all teeth may be lacking, those that exist may have malformations, maloclusions. Therefore prevention is of ut most importance in these patients, with special attention given to dental hygiene, control of tooth decay, regular check-ups, etc..The different options for treatment will be examined in order to obtain acceptable dental harmony, functioning and aesthetics.

Palabras clave : Incontinentia pigmenti; Bloch-Sulzberger syndrome; Dental agenesis; Prevention.

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