SciELO - Scientific Electronic Library Online

 
vol.46 número1Necrosis avascular de la epífisis proximal del primer metatarsiano en la infancia. Evolución a largo plazoMieloma múltiple con afectación laríngea: causa atípica de disfonía índice de autoresíndice de materiabúsqueda de artículos
Home Pagelista alfabética de revistas  

Servicios Personalizados

Revista

Articulo

Indicadores

Links relacionados

  • En proceso de indezaciónCitado por Google
  • No hay articulos similaresSimilares en SciELO
  • En proceso de indezaciónSimilares en Google

Compartir


Anales del Sistema Sanitario de Navarra

versión impresa ISSN 1137-6627

Resumen

MORENO-SANCHEZ, Amelia; MOLINA-HERRANZ, David; SANCHEZ-ANDRES, Armando  y  MONGE-GALINDO, Lorena. Intracranial hypotension syndrome in a pediatric patient with Marfan syndrome. Anales Sis San Navarra [online]. 2023, vol.46, n.1, e1031.  Epub 10-Jul-2023. ISSN 1137-6627.  https://dx.doi.org/10.23938/assn.1031.

Intracranial hypotension syndrome (IHS) is attributed to reduced cerebrospinal fluid (CSF) pressure. It may be spontaneous or secondary to a history of trauma or systemic disease.

We present the case of an 11-year-old boy, with medical history of Marfan syndrome, with orthostatic headache and persistent vomiting (12 hours) following a fall on the sacrococcygeal region. Magnetic resonance showed extradural fluid collections at dorsal and lumbosacral levels, compatible with CSF leak. The condition was resolved with treatment, but the patient had two new episodes during the follow-up period. Thus, an epidural blood patch was performed two years after the first episode.

Although HIS is uncommon in children, it should be suspected in patients with orthostatic headache, particularly if the patient presents a connectivopathy. Few studies have assessed the management of HIS in paediatric age. The case presented here and the reviewed available literature provides further data for these type of cases.

Palabras clave : Orthostatic headache; Intracranial hypotension; Fistula; Cerebrospinal fluid; Marfan syndrome.

        · resumen en Español     · texto en Español     · Español ( pdf )