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Neurocirugía
versión impresa ISSN 1130-1473
Resumen
CONDE, F.; LAZO, E.; LOURIDO, J. y DOMINGUEZ, J.. Cranial hemophilic pseudotumor. Neurocirugía [online]. 2006, vol.17, n.2, pp.158-161. ISSN 1130-1473.
The haemophilic pseudotumor is defined as an encased hematoma that increases of volume progressively by episodes of recurrent hemorrhage. It is a rare complication of haemophilia occurring in 1-2% of patients with moderate or severe factor Vlll or IX deficiency. Its more frequent location is in the long bones of low extremities and pelvis. We report a case of a 21-year-old man with moderate deficiency of factor VIII (19% of normal factor VIII activity) that developed a pseudotumor in the cranium. To our knowledge, this is the third case of the cranial hemophilic pseudotumor in medical literature.
Palabras clave : Pseudotumor; Haemophilia; Surgery.