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Anales de Medicina Interna

versão impressa ISSN 0212-7199

Resumo

OBON AZUARA, B.; GUTIERREZ CIA, I.  e  SANCHEZ POLO, C.. Non invasive mechanical ventilation in Intensive Care Unit in patient with respiratory failure as the first manifestation of dermatomyositis. An. Med. Interna (Madrid) [online]. 2005, vol.22, n.9, pp.434-436. ISSN 0212-7199.

Polymiositis and dermatomyositis are idiopathic inflammatory myositis with several respiratory complications but the acute failure respiratory is uncommon, and in the more severity types needs noninvasive mechanical ventilation.The case report a dermatomyositis patient who needed intensive care to failure respiratory due to muscle weakness who did not respond to corticoids -with pulsed prednisolone- in combination with another immunosuppressive agent with methotrexate, and after this with cyclofosfamide and cyclosporin. Along her stay in ICU is used a succesfully treatment with noninvasive mechanical ventilation and added high dose immunoglobulin intravenous, although there is a controversial about its use, was an effective treatment due to drug resistant dermatomyositis front to immunosuppression.

Palavras-chave : Dermatomyositis; ICU; Intensive Care Medicine; non invasive mechanical ventilation; Respiratory failure; dermatomyositis; Intravenous immunoglobulin.

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