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Archivos de la Sociedad Española de Oftalmología

versão impressa ISSN 0365-6691

Resumo

CESPEDES, A.; PEREZ-DE-ARCELUS, M.  e  GARCIA-ARUMI, J.. Best's vitelliform macular dystrophy associated with choroidal neovascularization. Arch Soc Esp Oftalmol [online]. 2012, vol.87, n.10, pp.333-336. ISSN 0365-6691.  https://dx.doi.org/10.1016/j.oftal.2011.11.010.

Case report: We report the case of a child with a sudden loss of vision of the left eye. Ophthalmoscopic examination revealed vitelliform lesions in both foveal centers, as well as an adjacent hemorrhage in his left eye. Fluorescein angiography confirmed the presence of a neovascular membrane in his left eye. The electrooculogram showed disease. According to complementary studies the patient was diagnosed with Best's disease associated with choroidal neovascularization. Discussion: The diagnosis of Best's vitelliform macular dystrophy is often a casual finding as visual acuity tends to remain stable for long periods of time. A sudden deterioration in vision may suggest complications, such as choroidal neovascularization.

Palavras-chave : Best's vitelliform macular dystrophy; Choroidal neovascularization; Electrooculogram.

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