Resumo

GONZALEZ, G. et al. Segmental odontomaxillary dysplasia. A rare pathology of dental interest: two case reports. Av Odontoestomatol [online]. 2014, vol.30, n.5, pp.243-250. ISSN 2340-3152.

We report two new cases of segmental odontomaxillary dysplasia (SOMD); a rare developmental pathology characterized by segmental maturation defects in bone, gingiva and teeth at one quadrant of the maxilla. It has three typical clinical signs: unilateral maxilla abnormality, ipsilateral gingival enlargement and one or two premolar agenesis, unusual in a first molar. Sometimes it´s associated with facial alterations: mucocutaneous indistinct upper lip border, unilateral pigmentation erythema, hypopigmentation of upper lip and hypertrichosis. Cases presented correspond to male and female patients. Both were diagnosed in adolescence; until present day are under orthodontic treatment in order to minimize the aesthetic and functional disorders caused by this pathology. The purpose of this article is to report two new cases to international registers, establishing the most relevant clinical and histopathological features and comparing them with published studies.

Palavras-chave : Hemimaxillary dysplasia; unilateral gingival enlargement; unilateral premolar agenesis; facial asymmetry; HATS.

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