Resumo

PINTO BONILLA, JC et al. Orbital affectation of Wegener’s granulomatosis. Arch Soc Esp Oftalmol [online]. 2004, vol.79, n.5, pp.243-246. ISSN 0365-6691.

Case report: Patient who consults for a recidivant orbital mass. Preliminary clinical and image studies suggested an initial differential diagnosis between a lachrymal gland tumor or an orbital located pseudotumor. However, the clinical evolution of the case required a re-evaluation of the preliminary diagnosis. The clinical, histologic and serologic findings were key in the final diagnosis. Discussion: Wegener´s granulomatosis is a necrotizing vasculitis. Classically it affects the upper airways, lungs and kidneys. Between 30% and 70% of patients present ophthalmic symptoms during the course of the illness. Ophthalmic affectation prior to systemic manifestations is less frequent and could delay final diagnosis.

Palavras-chave : Wegener´s granulomatosis; orbital pseudotumour; systemic vasculitis.