Resumo

INOSTROZA, María Antonieta  e  VERDUGO, Francisco Javier. Incontinentia pigmenti associated with cleft palate: report of a case. Rev Esp Cirug Oral y Maxilofac [online]. 2013, vol.35, n.2, pp.74-77. ISSN 2173-9161.  https://dx.doi.org/10.1016/j.maxilo.2011.07.006.

Incontinentia pigmenti (IP2, Block-Sulzberger Syndrome) is a rare x-linked dominant genodermatosis mainly affecting females. It consists of characteristic skin manifestations and dental, ocular, neurological, and other disorders. We present a case report with classical cutaneous features diagnosed with incontinentia pigmenti associated with a cleft palate.

Palavras-chave : Congenital Abnormalities; Dermatosis; Incontinentia pigmenti; Cleft palate.

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