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Anales de Medicina Interna

versión impresa ISSN 0212-7199

Resumen

VILLASANTE DE LA PUENTE, A. et al. Surconeal pustular dermatosis of Sneddon Wilkinson and myeloma. An. Med. Interna (Madrid) [online]. 2001, vol.18, n.7, pp.33-35. ISSN 0212-7199.

A case of subcorneal pustular dermatosis is described, this disease is not very common. Its origin remains unknown, there are some data that indicate an inmunological basis because of its associations to hematological disorders and others autoinmune diseases. The diagnosis is based on clinic suspects and the histopathological analysis. The differentiation among other dermatosis like pustular psoriasis, due to its therapeutic implication and evolution. This patient developed an IgA-K myeloma after nine years of evolution, a very common finding in this desease.It has not definitive treatment, being corticosteroids and sulfonamides more effective. The prognosis depends on the appearance of complications and associated processes. 

Palabras clave : Pustular dermatosis; Myeloma; Autoimmunity; Sulfonamides.

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