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Cirugía Plástica Ibero-Latinoamericana
versión On-line ISSN 1989-2055versión impresa ISSN 0376-7892
Resumen
GUTIERREZ GOMEZ, C. et al. Multiple tricoephitelioma. Cir. plást. iberolatinoam. [online]. 2012, vol.38, n.2, pp.163-167. ISSN 1989-2055. https://dx.doi.org/10.4321/S0376-78922012000200009.
Trichoepithelioma, first described by Brooke in 1892, also known as cystic adenoid epithelioma, is a dominantly inherited genodermatosis originated in the follicle bulb. There are two clinical forms, solitary and multiple. Some authors advocate not to treat them, but multiple trichoepithelioma presents a significant cosmetic problem and partial resection can lead to recurrence and excessive scarring, some cases with an aggressive behavior. We present a clinical case of multiple tricoepithelioma with severe deformity of the face in which we realized radical resection with restitution of anatomical units by local flaps. We consider that the multiple cases should be excised with total skin to avoid recurrence and obtain acceptable results.
Palabras clave : Trichoepithelioma; Cystic adenoid epithelioma; Anatomical units.