Abstract

DE LA CRUZ-REYES, S.; PALAFOX-HERNANDEZ, A.; FLORES-ALVAREZ, E.  and  OBREGON-MIMBELA, J.. Chondrosarcoma of the maxilla in pediatric patient. Cir. plást. iberolatinoam. [online]. 2014, vol.40, n.1, pp.93-98. ISSN 1989-2055.  https://dx.doi.org/10.4321/S0376-78922014000100013.

Chondrosarcoma is a malignant tumor of cartilaginous origin and unknown etiology, histologically characterized by a complete development of cartilaginous structures with no growth of bone. It represents approximately 10% of all bone neoplasms. It's usually presented in long bones, pelvis and ribs and it's extremely rare in craniofacial locations (less than 5%), where are considered more aggressive because of its rapid growth and a larger proportion of metastasis. When present in these locations, most affected sites in order of frequency are: maxilla, jaw, nasal septum and paranasal sinuses. The reported age ranges are 8 months to 75 years, with its peak incidence between the fifth and seventh decades of life. We present a female 7 year old patient, who presented a chondrosarcoma in the maxilla, bulky and recurrent. Her initial clinical presentation was a nodular right gingival asymptomatic lesion, with slow growth and ongoing for 8 months. Computed tomography showed a 3 x 3 cm tumor in the right maxilla that underwent limited resection; the specimen was reported as a grade II chondrosarcoma that developed recurrence in a year. She received 9 chemotherapy cycles and later, bilateral subtotal maxillectomy and pallatectomy and initial reconstruction with titanium miniplates and alloplastic prostheses. We present photographs of initial assessment, additional imaging studies, histopathology, surgical procedure and postoperative state.

Keywords : Chondrosarcoma; Head and neck tumors; Tumors at pediatric age.

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