<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1139-7632</journal-id>
<journal-title><![CDATA[Pediatría Atención Primaria]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Pediatr Aten Primaria]]></abbrev-journal-title>
<issn>1139-7632</issn>
<publisher>
<publisher-name><![CDATA[Asociación Española de Pediatría de Atención Primaria]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1139-76322016000300018</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Manejo terapéutico de la atresia de vías biliares]]></article-title>
<article-title xml:lang="en"><![CDATA[Therapeutic management of biliary atresia]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Crehuet Gramatyka]]></surname>
<given-names><![CDATA[David]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Navarro Rubio]]></surname>
<given-names><![CDATA[Gemma]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Corporación Sanitaria y Universitaria Parc Taulí Unidad Docente Parc Taulí ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad Autònoma de Barcelona Facultad de Medicina ]]></institution>
<addr-line><![CDATA[Barcelona Barcelona]]></addr-line>
<country>Spain</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>09</month>
<year>2016</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>09</month>
<year>2016</year>
</pub-date>
<volume>18</volume>
<numero>71</numero>
<fpage>e141</fpage>
<lpage>e147</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_arttext&amp;pid=S1139-76322016000300018&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_abstract&amp;pid=S1139-76322016000300018&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_pdf&amp;pid=S1139-76322016000300018&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen La atresia de vías biliares es una enfermedad de origen desconocido que causa ictericia neonatal. Es la primera causa de trasplante hepático en niños (40%). Esto es debido a que su técnica correctora, la portoenterostomía de Kasai (KPE), únicamente consigue el drenaje biliar en aproximadamente un 60% de los casos. A pesar del correcto drenaje, solo un 20% llega a edad adulta con su hígado nativo, y una gran parte de ellos con complicaciones hepáticas y calidad de vida subóptima. Estos datos hacen replantearse continuamente el manejo terapéutico y si el trasplante podría ser el tratamiento de elección. El objetivo de esta revisión es actualizar la información disponible con el fin de determinar la mejor estrategia en su manejo. Partiendo de la base bibliográfica ya seleccionada, se realizó una búsqueda con los términos "biliary atresia" y "treatment". Debido a que el trasplante hepático a edades tempranas implica peores resultados, actualmente se prefiere la KPE como primera elección y el trasplante como tratamiento de rescate.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract Biliary atresia is a bile duct disease of unknown origin that causes neonatal jaundice. It is the leading cause of liver transplantation in children, accounting for 40%. This is because the corrective technique, Kasai portoenterostomy (KPE), biliary drainage gets only about 60% of cases. Despite proper drainage, 20% reach adulthood with their native liver, and a large part of them with liver complications and suboptimal quality of life. These data continuously rethink the therapeutic management of this disease and if the transplant could be the treatment of choice. The objective of this review is to update scientific information in order to determine the best strategy in managing the disease. From the bibliographic, a search was conducted with the terms "biliary atresia" and "treatment". Due to liver transplantation at an early age means worse, today most scientific information supports the KPE as first choice and transplantation as secundary therapy]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Atresia biliar]]></kwd>
<kwd lng="es"><![CDATA[Tratamiento]]></kwd>
<kwd lng="en"><![CDATA[Biliary atresia]]></kwd>
<kwd lng="en"><![CDATA[Treatment]]></kwd>
</kwd-group>
</article-meta>
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</name>
</person-group>
<article-title xml:lang=""><![CDATA[Redo surgery for biliary atresia]]></article-title>
<source><![CDATA[Pediatr Surg Int]]></source>
<year>2013</year>
<volume>29</volume>
<page-range>989-93</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
