<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1139-7632</journal-id>
<journal-title><![CDATA[Pediatría Atención Primaria]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Pediatr Aten Primaria]]></abbrev-journal-title>
<issn>1139-7632</issn>
<publisher>
<publisher-name><![CDATA[Asociación Española de Pediatría de Atención Primaria]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1139-76322017000400011</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Alagille; una patología que tener en cuenta]]></article-title>
<article-title xml:lang="en"><![CDATA[Alagille syndrome. A pathology to be considered]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ortega Pérez]]></surname>
<given-names><![CDATA[SN]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[González Santana]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ramos Varela]]></surname>
<given-names><![CDATA[JC]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cañizo Fernández]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Peña Quintana]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,CS de Arucas  ]]></institution>
<addr-line><![CDATA[ Gran Canaria]]></addr-line>
<country>España</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Hospital Universitario Materno-Infantil de Canarias Servicio de Gastroenterología, Hepatología y Nutrición pediátrica ]]></institution>
<addr-line><![CDATA[ Gran Canaria]]></addr-line>
<country>España</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Universitario Materno-Infantil de Canarias Servicio de Gastroenterología, Hepatología y Nutrición pediátrica ]]></institution>
<addr-line><![CDATA[ Gran Canaria]]></addr-line>
<country>España</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,CS de Arucas  ]]></institution>
<addr-line><![CDATA[ Gran Canaria]]></addr-line>
<country>España</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Hospital Universitario Materno-Infantil de Canarias Servicio de Gastroenterología, Hepatología y Nutrición pediátrica ]]></institution>
<addr-line><![CDATA[ Gran Canaria]]></addr-line>
<country>España</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>09</month>
<year>2017</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>09</month>
<year>2017</year>
</pub-date>
<volume>19</volume>
<numero>75</numero>
<fpage>267</fpage>
<lpage>270</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_arttext&amp;pid=S1139-76322017000400011&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_abstract&amp;pid=S1139-76322017000400011&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_pdf&amp;pid=S1139-76322017000400011&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: El síndrome de Alagille es una patología poco frecuente. Afecta a uno de cada 100 000 recién nacidos vivos. Se caracteriza por una hipoplasia de vías biliares que se asocia a otras malformaciones. Se presenta el caso de un niño chino de cuatro años al que se le diagnosticó esta patología tras ser adoptado a los 11 meses de edad.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract: Alagille syndrome is an uncommon pathology. It is found in 1/100,000 live births. It is characterized by biliary duct hypoplasia associated with other malformations. We report the case of a four-year-old Chinese child who was diagnosed with this pathology after being adopted at 11 months of age.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Alagille]]></kwd>
<kwd lng="es"><![CDATA[Enfermedades de los conductos biliares]]></kwd>
<kwd lng="es"><![CDATA[Colestasis]]></kwd>
<kwd lng="en"><![CDATA[Alagille syndrome]]></kwd>
<kwd lng="en"><![CDATA[Bile duct diseases]]></kwd>
<kwd lng="en"><![CDATA[Cholestasis]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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