<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1139-7632</journal-id>
<journal-title><![CDATA[Pediatría Atención Primaria]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Pediatr Aten Primaria]]></abbrev-journal-title>
<issn>1139-7632</issn>
<publisher>
<publisher-name><![CDATA[Asociación Española de Pediatría de Atención Primaria]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1139-76322018000100003</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Revisión clínica y diagnóstica de la enfermedad de Kawasaki: estudio descriptivo, retrospectivo y analítico]]></article-title>
<article-title xml:lang="en"><![CDATA[Review of the diagnosis and clinical features of Kawasaki disease: retrospective descriptive and analytical study]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Baleato Gómez]]></surname>
<given-names><![CDATA[Beatriz]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[González Ávila]]></surname>
<given-names><![CDATA[Carmen]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Souto Cainzos]]></surname>
<given-names><![CDATA[Borja]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Iglesias González]]></surname>
<given-names><![CDATA[Beatriz]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[González Menchén]]></surname>
<given-names><![CDATA[Cristina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ramos Amador]]></surname>
<given-names><![CDATA[José Tomás]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Clínico Universitario San Carlos Servicio de Pediatría ]]></institution>
<addr-line><![CDATA[Madrid ]]></addr-line>
<country>España</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2018</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2018</year>
</pub-date>
<volume>20</volume>
<numero>77</numero>
<fpage>15</fpage>
<lpage>24</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_arttext&amp;pid=S1139-76322018000100003&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_abstract&amp;pid=S1139-76322018000100003&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_pdf&amp;pid=S1139-76322018000100003&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[ Introducción:  la enfermedad de Kawasaki es una vasculitis aguda, febril y autolimitada, que puede complicarse con alteraciones cardiovasculares. Su diagnóstico se basa en criterios clínicos. A pesar de un tratamiento eficaz, es la principal causa de cardiopatía adquirida en niños de países desarrollados.  Objetivos:  analizar la prevalencia de alteraciones coronarias en pacientes pediátricos diagnosticados en nuestro medio; evaluar las características demográficas, clínicas y analíticas de la población de estudio y describir los factores de riesgo de alteración coronaria en niños con enfermedad de Kawasaki.  Métodos:  se revisaron de forma retrospectiva las historias clínicas de los niños diagnosticados de enfermedad de Kawasaki desde enero de 1997 hasta diciembre de 2016 en el Hospital Clínico San Carlos (Madrid, España). Se consideró diagnóstico de enfermedad de Kawasaki la presencia de los criterios clínicos propuestos por la Academia Americana de Pediatría en 2017.  Resultados:  la enfermedad de Kawasaki se presentó fundamentalmente durante el invierno (n = 13; 56,5%) en mujeres (n = 12; 52,2%) de cinco años o menos (n = 18; 78,3%), que desarrollaron fiebre (n = 23; 100%) junto con cambios en la mucosa orofaríngea (n = 21; 91,3%) y presentaron proteína C reactiva y velocidad de sedimentación globular elevadas (n = 20; 86,95% y n = 13; 86,6%). Fueron tratados con inmunoglobulina intravenosa (n = 22; 95,7%) y ácido acetilsalicílico a dosis antiinflamatoria (n = 22; 95,7%) o antiagregante (n = 20; 87%). Tres pacientes (13%) desarrollaron alteraciones coronarias, que terminaron remitiendo.  Conclusiones:  en nuestra cohorte, la prevalencia de alteraciones coronarias fue similar a la reportada en nuestro medio y superior a la descrita en estudios internacionales. Los factores de riesgo de alteración coronaria son predominantemente niños con retraso en el diagnóstico y tratamiento, leucocitosis &gt;12 000/ul, proteína C reactiva &gt;3 mg/dl y trombocitosis.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ Introduction:  Kawasaki disease is an acute, febrile and self-limiting vasculitis that may be complicated by cardiovascular changes. Its diagnosis is based on clinical criteria. Although effective treatment is available, it is the leading cause of acquired heart disease in children in developed countries.  Objectives:  to assess the prevalence of coronary artery abnormalities in paediatric patients diagnosed in our area, and the demographic, clinical and laboratory characteristics of the population under study, describing the risk factors for coronary involvement in children with Kawasaki disease.  Methods:  we performed a retrospective review of the medical records of children given a diagnosis of Kawasaki disease between January 1997 and December 2016 at the Hospital Clínico San Carlos (Madrid, Spain). We defined Kawasaki disease as the presence of the clinical criteria proposed for its diagnosis by the American Academy of Pediatrics in 2017.  Results:  cases of Kawasaki disease were most frequent in the winter (n = 13; 56.5%), in girls (n = 12; 52.2%) and in children aged 5 years or less (n = 18; 78.3%). Patients presented with fever (n = 23; 100%) and changes in the oropharyngeal mucosa (n = 21; 91.3%), with elevation of C-reactive protein and the erythrocyte sedimentation rate (n = 20; 86.95% and n = 13; 86.6%). Treatment consisted of intravenous immunoglobulin (n = 22; 95.7%) and acetylsalicylic acid at anti-inflammatory doses (n = 22; 95.7%) or antithrombotic doses (n = 20; 87%). Three patients (13%) developed coronary artery abnormalities that eventually resolved.  Conclusions:  in our cohort, the prevalence of coronary complications was similar to the prevalence reported for Spain and higher than the prevalence reported in international studies. The main risk factors for coronary artery abnormalities were delays in diagnosis or treatment, a white blood cell count greater than 12 000 cells/µl, a serum level of C-reactive protein greater than 3 mg/dl and thrombocytosis.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Factores de riesgo]]></kwd>
<kwd lng="es"><![CDATA[Enfermedad coronaria]]></kwd>
<kwd lng="es"><![CDATA[Síndrome mucocutáneo linfonodular]]></kwd>
<kwd lng="en"><![CDATA[Risk factors]]></kwd>
<kwd lng="en"><![CDATA[Coronary disease]]></kwd>
<kwd lng="en"><![CDATA[Mucocutaneous lymph node syndrome]]></kwd>
</kwd-group>
</article-meta>
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