<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1139-7632</journal-id>
<journal-title><![CDATA[Pediatría Atención Primaria]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Pediatr Aten Primaria]]></abbrev-journal-title>
<issn>1139-7632</issn>
<publisher>
<publisher-name><![CDATA[Asociación Española de Pediatría de Atención Primaria]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1139-76322018000400006</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[¿Qué puede ocultar una mancha café con leche?]]></article-title>
<article-title xml:lang="en"><![CDATA[What can hide a café-au-lait skin pigmentation?]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Morata Alba]]></surname>
<given-names><![CDATA[Júlia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Morata Alba]]></surname>
<given-names><![CDATA[Laia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Díez Gandía]]></surname>
<given-names><![CDATA[Eva]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Lluís Alcanyís Servicio de Pediatría. ]]></institution>
<addr-line><![CDATA[Játiva Valencia]]></addr-line>
<country>España</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Centro de Salud Enguera  ]]></institution>
<addr-line><![CDATA[Enguera Valencia]]></addr-line>
<country>España</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Hospital Lluís Alcanyís  ]]></institution>
<addr-line><![CDATA[Játiva Valencia]]></addr-line>
<country>España</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2018</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2018</year>
</pub-date>
<volume>20</volume>
<numero>80</numero>
<fpage>371</fpage>
<lpage>374</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_arttext&amp;pid=S1139-76322018000400006&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_abstract&amp;pid=S1139-76322018000400006&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_pdf&amp;pid=S1139-76322018000400006&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen El síndrome McCune-Albright es una enfermedad rara de carácter esporádico, descrita por McCune y Albright en 1937. Está causada por la mutación del gen GNAS1, que estimula el crecimiento y la función de las glándulas endocrinas, los melanocitos y los osteoclastos. Tríada característica de displasia fibrosa poliostótica, alteraciones endocrinas múltiples y mancha café con leche.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract McCune-Albright syndrome is a rare sporadic disease, described by McCune and Albright in 1937. It is caused by the mutation of the GNAS1 gene, which stimulates the growth and function of the endocrine glands, melanocytes and osteoclasts. Triad characteristic: polyostotic fibrous dysplasia, multiple endocrine alterations and café-au-lait skin pigmentation.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Displasia fibrosa]]></kwd>
<kwd lng="es"><![CDATA[Mancha café con leche]]></kwd>
<kwd lng="es"><![CDATA[Síndrome de McCune-Albright]]></kwd>
<kwd lng="en"><![CDATA[Fibrous dysplasia]]></kwd>
<kwd lng="en"><![CDATA[Café-au-lait skin pigmentation]]></kwd>
<kwd lng="en"><![CDATA[McCune-Albright syndrome]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Dean]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[McCune-Albright Syndrome]]></article-title>
<person-group person-group-type="editor">
<name>
<surname><![CDATA[Pratt]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[McLeod]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Dean]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Malheiro]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Rubinstein]]></surname>
<given-names><![CDATA[W]]></given-names>
</name>
</person-group>
<source><![CDATA[Medical Genetics Summaries]]></source>
<year></year>
</nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Raus]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
<name>
<surname><![CDATA[Coroiu]]></surname>
<given-names><![CDATA[RE]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[McCune Albright syndrome - association of fibrous dysplasia, café-au-lait skin spots and hyperthyroidism - case report]]></article-title>
<source><![CDATA[Clujul Med]]></source>
<year>2016</year>
<volume>89</volume>
<page-range>559-64</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Cho]]></surname>
<given-names><![CDATA[EK]]></given-names>
</name>
<name>
<surname><![CDATA[Kim]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Yang]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Ki]]></surname>
<given-names><![CDATA[CS]]></given-names>
</name>
<name>
<surname><![CDATA[Lee]]></surname>
<given-names><![CDATA[JE]]></given-names>
</name>
<name>
<surname><![CDATA[Cho]]></surname>
<given-names><![CDATA[SY]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Clinical and endocrine characteristics and genetic analysis of Korean children with McCune-Albright syndrome: a retrospective cohort study]]></article-title>
<source><![CDATA[Orphanet J Rare Dis]]></source>
<year>2016</year>
<volume>11</volume>
<page-range>113</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Agopiantz]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Journeau]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Lebon-Labich]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Sorlin]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Cuny]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Weryha]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Leheup]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[McCune-Albright syndrome, natural history and multidisciplinary management in a series of 14 pediatric cases]]></article-title>
<source><![CDATA[Ann Endocrinol (Paris)]]></source>
<year>2016</year>
<volume>77</volume>
<page-range>7-13</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
