<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1889-836X</journal-id>
<journal-title><![CDATA[Revista de Osteoporosis y Metabolismo Mineral]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Osteoporos Metab Miner]]></abbrev-journal-title>
<issn>1889-836X</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Española de Investigaciones Óseas y Metabolismo Mineral]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1889-836X2022000400005</article-id>
<article-id pub-id-type="doi">10.4321/s1889-836x2022000400005</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Utilidad del trabecular bone score en sujetos adultos con osteogénesis imperfecta]]></article-title>
<article-title xml:lang="en"><![CDATA[Usefulness of the trabecular bone score in adult subjects with osteogenesis imperfecta]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Florez]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
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<contrib contrib-type="author">
<name>
<surname><![CDATA[Muxi]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
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</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[González]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
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<contrib contrib-type="author">
<name>
<surname><![CDATA[Monegal]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
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<contrib contrib-type="author">
<name>
<surname><![CDATA[Guañabens]]></surname>
<given-names><![CDATA[N]]></given-names>
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<contrib contrib-type="author">
<name>
<surname><![CDATA[Peris]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
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</contrib-group>
<aff id="A01">
<institution><![CDATA[,Universitat de Barcelona Instituto de Investigaciones Biomédicas August Pi i Sunyer, Centro de Investigación Biomédica en Red en el Área temática de Enfermedades Hepáticas Hospital Clínic. Servicio de Reumatología. Unidad de Patología Metabólica Ósea]]></institution>
<addr-line><![CDATA[Barcelona ]]></addr-line>
<country>España</country>
</aff>
<aff id="A02">
<institution><![CDATA[,Hospital Clínic Servicio de Medicina Nuclear ]]></institution>
<addr-line><![CDATA[Barcelona ]]></addr-line>
<country>España</country>
</aff>
<aff id="A03">
<institution><![CDATA[,Hospital Clínic Laboratorio de Inmunología ]]></institution>
<addr-line><![CDATA[Barcelona ]]></addr-line>
<country>España</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2022</year>
</pub-date>
<volume>14</volume>
<numero>4</numero>
<fpage>125</fpage>
<lpage>130</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_arttext&amp;pid=S1889-836X2022000400005&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_abstract&amp;pid=S1889-836X2022000400005&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_pdf&amp;pid=S1889-836X2022000400005&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Objetivo: Analizar la utilidad del trabecular bone score (TBS) en adultos con osteogénesis imperfecta (OI) y su relación con variables clínicas, antropométricas y densitométricas, especialmente con la presencia de fracturas y la severidad de la enfermedad.  Material y métodos: Estudio transversal realizado en 31 pacientes adultos con OI (edad 40.5±15.2 años, 68% mujeres, 87% tipo I). Se analizaron las características clínicas de los pacientes (fracturas, tipo de OI, IMC y tratamiento), la densidad mineral ósea (DMO) (mediante DXA), valorando la presencia de osteoporosis densitométrica, y los valores de TBS (TBS iNsight), estimando la presencia de microarquitectura degradada (valores &lt;1.230). Los resultados se compararon entre los diferentes tipos de OI (I y III-IV) y con los de un grupo control de sujetos sanos.  Resultados: La mayoría de los pacientes (29/31, 94%) tenían antecedentes de fracturas y el 29% recibía tratamiento antiosteoporótico. El 61% tenía una osteoporosis densitométrica y el 19% tenían una microarquitectura degradada. No se observaron diferencias en los valores del TBS según la gravedad de la OI (OI tipo I vs. III-IV: 1.297 vs. 1.339, p=n.s.); ningún paciente con OI tipo III-IV tenía TBS&lt;1.230. Los valores de TBS se relacionaron con la edad (r=-0.6, p&lt;0.01), la DMO lumbar (r=0.4, p=0.03) y el IMC (r=-0.5, p=0.01). Los pacientes con OI tenían valores más bajos de TBS y DMO que el grupo control en todas las localizaciones analizadas.  Conclusión: El TBS es poco sensible en la valoración de la calidad ósea en la OI, pues ninguno de los pacientes con OI grave tenía una microarquitectura degradada y ésta sólo se observó en el 19% de los pacientes con OI a pesar de presentar una alta prevalencia de fracturas.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Summary  Objective: To analyze the usefulness of the trabecular bone score (TBS) in adults with osteogenesis imperfecta (OI) and its relationship with clinical, anthropometric and densitometric variables, especially with the presence of fractures and the severity of the disease.  Material and methods: Cross-sectional study conducted in 31 adult patients with OI (age 40.5±15.2 years, 68% women, 87% type I). The clinical characteristics of the patients (fractures, type of OI, BMI and treatment), bone mineral density (BMD) (using DXA), assessing the presence of densitometric osteoporosis, and TBS values (TBS iNsight), estimating the presence of degraded microarchitecture (values &lt;1.230). The results were compared between the different OI types (I and III-IV) and with those of a control group of healthy subjects.  Results: Most of the patients (29/31, 94%) had a history of fractures and 29% received antiosteoporotic treatment. 61% had densitometric osteoporosis and 19% had degraded microarchitecture. No differences were observed in the TBS values according to OI severity (OI type I vs. III-IV: 1,297 vs. 1,339, p=n.s.); no patient with OI type III-IV had TBS &lt;1230. TBS values were related to age (r=-0.6, p&lt;0.01), lumbar BMD (r=0.4, p=0.03) and BMI (r=-0.5 , p=0.01). Patients with OI had lower values of TBS and BMD than the control group in all locations analyzed.  Conclusions: TBS is not very sensitive in assessing bone quality in OI, since none of the patients with severe OI had a degraded microarchitecture and this was only observed in 19% of patients with OI despite presenting a high prevalence of fractures.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[osteogénesis imperfecta]]></kwd>
<kwd lng="es"><![CDATA[trabecular bone score]]></kwd>
<kwd lng="es"><![CDATA[TBS]]></kwd>
<kwd lng="en"><![CDATA[osteogenesis imperfecta]]></kwd>
<kwd lng="en"><![CDATA[trabecular bone score]]></kwd>
<kwd lng="en"><![CDATA[TBS]]></kwd>
</kwd-group>
</article-meta>
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