<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2695-5075</journal-id>
<journal-title><![CDATA[Iberoamerican Journal of Medicine]]></journal-title>
<abbrev-journal-title><![CDATA[Iberoam J Med]]></abbrev-journal-title>
<issn>2695-5075</issn>
<publisher>
<publisher-name><![CDATA[Hospital San Pedro]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2695-50752021000200010</article-id>
<article-id pub-id-type="doi">10.5281/zenodo.4483765</article-id>
<title-group>
<article-title xml:lang="en"><![CDATA[Rubinstein-Taybi syndrome: principal oral and dental disorders and literature update]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[de la Parte-Serna]]></surname>
<given-names><![CDATA[Alejandro Carlos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Ortega-Soria]]></surname>
<given-names><![CDATA[Ricardo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Oliván-Gonzalvo]]></surname>
<given-names><![CDATA[Gonzalo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,University of Zaragoza Faculty of Health and Sports Sciences ]]></institution>
<addr-line><![CDATA[Huesca ]]></addr-line>
<country>España</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,HLA Hospital Montpellier Pediatrics Emergency Service ]]></institution>
<addr-line><![CDATA[Zaragoza ]]></addr-line>
<country>España</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Social Services Institute of Aragón  ]]></institution>
<addr-line><![CDATA[Zaragoza ]]></addr-line>
<country>España</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2021</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2021</year>
</pub-date>
<volume>3</volume>
<numero>2</numero>
<fpage>169</fpage>
<lpage>172</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_arttext&amp;pid=S2695-50752021000200010&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_abstract&amp;pid=S2695-50752021000200010&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_pdf&amp;pid=S2695-50752021000200010&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Introduction: Oral and dental (OD) disorders in children with Rubinstein-Taybi syndrome (RTS) are frequent but not well-known by dentists and pediatricians due to the syndrome being extremely rare.  Objective: To describe the OD findings observed in a 5-year-old girl with RTS and to update the literature.  Clinical case: The patient presented the following OD manifestations: prominent lower lip, narrow mouth opening, narrow and arched palate, history of angular cheilitis, micrognathia, poor lingual motility, plaque and tartar, bleeding from gingival areas due to poor dental prophylaxis, and malocclusion in the form of an anterior open bite. These OD manifestations are seen in more than 40-60% of patients with RTS.  Conclusions: Professionals who treat children with RTS should become aware of the advisability of referring them to the pediatric dentist from 1 year of age and performing check-ups every 6 months. Dental management is often difficult so collaboration with anesthesiologists is recommended in order to carry out a safe and effective treatment.]]></p></abstract>
<kwd-group>
<kwd lng="en"><![CDATA[Rubinstein-Taybi syndrome]]></kwd>
<kwd lng="en"><![CDATA[Odontostomatology disorders]]></kwd>
<kwd lng="en"><![CDATA[Pediatric dentistry]]></kwd>
<kwd lng="en"><![CDATA[Disabled persons]]></kwd>
<kwd lng="en"><![CDATA[Determination of healthcare needs]]></kwd>
<kwd lng="en"><![CDATA[Special patients]]></kwd>
<kwd lng="en"><![CDATA[Talon cusps]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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