<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1130-0558</journal-id>
<journal-title><![CDATA[Revista Española de Cirugía Oral y Maxilofacial]]></journal-title>
<abbrev-journal-title><![CDATA[Rev Esp Cirug Oral y Maxilofac]]></abbrev-journal-title>
<issn>1130-0558</issn>
<publisher>
<publisher-name><![CDATA[ Sociedad Española de Cirugía Oral y Maxilofacial y de Cabeza y Cuello]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1130-05582019000100041</article-id>
<article-id pub-id-type="doi">10.20986/recom.2019.1030/2019</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Sarcoma mieloide intraoral: forma poco común de debut de la leucemia aguda mieloide]]></article-title>
<article-title xml:lang="en"><![CDATA[Intraoral myeloid sarcoma. An uncommon debut of acute myeloid leukemia]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vázquez-Martínez]]></surname>
<given-names><![CDATA[Cristina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Redondo-Alamillos]]></surname>
<given-names><![CDATA[Marta]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Romance-García]]></surname>
<given-names><![CDATA[Ana-I.]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sánchez-Aniceto]]></surname>
<given-names><![CDATA[Gregorio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Universitario 12 de Octubre Servicio de Cirugía Oral y Maxilofacial ]]></institution>
<addr-line><![CDATA[Madrid ]]></addr-line>
<country>España</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>03</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>03</month>
<year>2019</year>
</pub-date>
<volume>41</volume>
<numero>1</numero>
<fpage>41</fpage>
<lpage>43</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_arttext&amp;pid=S1130-05582019000100041&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_abstract&amp;pid=S1130-05582019000100041&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.isciii.es/scielo.php?script=sci_pdf&amp;pid=S1130-05582019000100041&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN La leucemia aguda mieloide (LAM) es una neoplasia maligna con manifestaciones sistémicas, pudiendo presentar lesiones a nivel intraoral. Es el cáncer más frecuente en la infancia y constituye la primera causa de muerte por cáncer en la edad pediátrica. El sarcoma mieloide es un tumor maligno extramedular compuesto por células precursoras mieloides inmaduras. Este tumor se asocia fundamentalmente con la leucemia mieloide aguda y síndromes mielodisplásicos y, generalmente, debuta después del diagnóstico de la enfermedad primaria. La aparición del sarcoma mieloide dentro de la cavidad oral como manifestación inicial de la LAM es extremadamente rara (3-6 % de los casos según las series). Se presenta el caso de una lactante de 19 meses de edad que llevaron a Urgencias por fiebre y una tumoración gingival en el cuarto cuadrante refractaria a tratamiento antibiótico. Se solicitó un estudio ecográfico para valorar la existencia de un absceso, donde se identificó una lesión que, tras realizar una biopsia para estudio anatomopatológico, resultó ser un sarcoma mieloide. La paciente fue diagnosticada de LAM y se inició tratamiento quimioterápico. Tras tres ciclos, actualmente la paciente se encuentra libre de enfermedad.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Acute myeloid leukemia (AML) is a malignant neoplasm with systemic manifestations, which may present intraoral lesions. It is the most common cancer in childhood and the leading cause of death from cancer in pediatric population. Myeloid sarcoma is a malignant extramedullary tumor composed of immature myeloid precursor cells. This tumor is mainly associated with AML and myelodysplastic syndromes and, generally, shows up after the diagnosis of the primary disease. The appearance of myeloid sarcoma within the oral cavity as an initial manifestation of AMK is extremely rare (3-6% of cases according to the series). We present a case of a 19-month infant who was taken to the Emergency Department due to fever and a gingival lesion that did not respond to antibiotic treatment. An ultrasound study was requested to assess the presence of an abscess. However, a lesion was identified and after performing a biopsy, pathologist found it was a myeloid sarcoma. The patient was diagnosed with AML and chemotherapy treatment was started. After three cycles of treatment, the patient is currently free of disease.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Leucemia aguda mieloide]]></kwd>
<kwd lng="es"><![CDATA[sarcoma mieloide]]></kwd>
<kwd lng="es"><![CDATA[neoplasia cavidad oral]]></kwd>
<kwd lng="en"><![CDATA[Acute myeloid leukemia]]></kwd>
<kwd lng="en"><![CDATA[myeloid sarcoma]]></kwd>
<kwd lng="en"><![CDATA[oral neoplasm]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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